Case 787 Sudden Death in Hemochromatosis after Closed-Chest Catheter Ablation of the Atrioventricular Junction

Robert Lemery; Pedro Brugada; Michael Havenith; Deborah Barbour; William C. Roberts; Hein J.J. Wellens

doi:10.1201/9781003409304-25

Case 787 Sudden Death in Hemochromatosis after Closed-Chest Catheter Ablation of the Atrioventricular Junction

Robert Lemery, Pedro Brugada, Michael Havenith, Deborah Barbour, William C. Roberts, Hein J.J. Wellens

Research output: Chapter in Book/Report/Conference proceeding › Chapter › Academic

Abstract

An active, healthy, and symptom free 16 year old boy with a family history of hypertrophic cardiomyopathy died suddenly while walking home from school. Necropsy showed absence of left ventricular hypertrophy (that is, normal heart weight), though the characteristic histological abnormalities of hypertrophic cardiomyopathy, such as cardiac muscle cell disorganisation and abnormal intramural coronary arteries, were present. It is likely that this patient had hypertrophic cardiomyopathy and died before left ventricular hypertrophy developed.

Original language	English
Title of host publication	Case Reports in Cardiology
Subtitle of host publication	Cardiomyopathy
Editors	William C. Roberts
Publisher	CRC Press
Pages	141-144
Number of pages	4
Edition	1
ISBN (Electronic)	9781000991819
ISBN (Print)	9781032529394
DOIs	https://doi.org/10.1201/9781003409304-25
Publication status	Published - 1 Jan 2023

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10.1201/9781003409304-25Licence: CC BY

Cite this

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title = "Case 787 Sudden Death in Hemochromatosis after Closed-Chest Catheter Ablation of the Atrioventricular Junction",

abstract = "An active, healthy, and symptom free 16 year old boy with a family history of hypertrophic cardiomyopathy died suddenly while walking home from school. Necropsy showed absence of left ventricular hypertrophy (that is, normal heart weight), though the characteristic histological abnormalities of hypertrophic cardiomyopathy, such as cardiac muscle cell disorganisation and abnormal intramural coronary arteries, were present. It is likely that this patient had hypertrophic cardiomyopathy and died before left ventricular hypertrophy developed.",

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AU - Brugada, Pedro

AU - Havenith, Michael

AU - Barbour, Deborah

AU - Roberts, William C.

AU - Wellens, Hein J.J.

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AB - An active, healthy, and symptom free 16 year old boy with a family history of hypertrophic cardiomyopathy died suddenly while walking home from school. Necropsy showed absence of left ventricular hypertrophy (that is, normal heart weight), though the characteristic histological abnormalities of hypertrophic cardiomyopathy, such as cardiac muscle cell disorganisation and abnormal intramural coronary arteries, were present. It is likely that this patient had hypertrophic cardiomyopathy and died before left ventricular hypertrophy developed.

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