PULMONARY ALVEOLAR PROTEINOSIS: ANOTHER AUTOIMMUNE DISEASE ASSOCIATED WITH SARCOIDOSIS?

Eda Burcu Boerner, Ulrich Costabel, Thomas Ernst Wessendorf, Dirk Theegarten, Martin Hetzel, Marjolein Drent, Francesco Bonella*

*Corresponding author for this work

Research output: Contribution to journalArticleAcademicpeer-review

Abstract

Pulmonary alveolar proteinosis (PAP) is a rare lung disease characterized by the accumulation of surfactant phospholipids and lipoproteins within the alveoli. Here we report on a female patient who was diagnosed with autoimmune PAP and successfully treated with whole lung lavage (WLL). 15 months after PAP diagnosis the patient developed marked fatigue. Additional tests revealed the diagnosis of sarcoidosis. We can only speculate that PAP and sarcoidosis in our patient are linked to each other based on the fact that other autoimmune disorders have also been associated with sarcoidosis.
Original languageEnglish
Pages (from-to)90-94
Number of pages5
JournalSarcoidosis Vasculitis and Diffuse Lung Diseases
Volume33
Issue number1
Publication statusPublished - 2016

Keywords

  • pulmonary alveolar proteinosis (PAP)
  • sarcoidosis
  • whole lung lavage

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