Modest proteasomal inhibition by aberrant ubiquitin exacerbates aggregate formation in a Huntington disease mouse model

Remko de Pril, Barbara Hobo, Paula van Tijn, Raymund A. C. Roos, Fred W. van Leeuwen*, David F. Fischer

*Corresponding author for this work

Research output: Contribution to journalArticleAcademicpeer-review

14 Citations (Web of Science)
Original languageEnglish
Pages (from-to)281-286
JournalMolecular and Cellular Neuroscience
Issue number3
Publication statusPublished - Mar 2010


  • Polyglutamine disease
  • Ubiquitin proteasome system
  • Neurodegeneration
  • Transgenic mice
  • Inclusions
  • Huntingtin

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