TY - JOUR
T1 - Management of congenital ichthyoses
T2 - Guidelines of care: Part Two: 2024 Update
AU - Mazereeuw-Hautier, Juliette
AU - Paller, Amy S
AU - O'Toole, Edel
AU - Dreyfus, Isabelle
AU - Bodemer, Christine
AU - Akiyama, Masashi
AU - Diociaiuti, Andrea
AU - El Hachem, Maya
AU - Fischer, Judith
AU - Gonzalez-Sarmiento, Rogelio
AU - Gutiérrez-Cerrajero, Carlos
AU - Ott, Hagen
AU - Has, Cristina
AU - Jonca, Nathalie
AU - Granier Tournier, Céline
AU - Martinez, Ana
AU - Traupe, Heiko
AU - Salavastru, Carmen Maria
AU - Schmuth, Matthias
AU - Sprecher, Eli
AU - Giehl, Kathrin
AU - Aldwin, Mandy
AU - Anton Morales, Ruth
AU - Santos, Saturnino
AU - Morren, Marie-Anne
AU - Audouze, Anne
AU - Malhotra, Raman
AU - Veldman, Karin
AU - Narbutt, Joanna
AU - Süßmuth, Kira
AU - Gostynski, Antoni
AU - Hernandez-Martin, Angela
PY - 2025/4/7
Y1 - 2025/4/7
N2 - In 2019, a group of experts published the first European guidelines for the management of congenital ichthyoses after a multidisciplinary expert meeting held in 2016. An update of these guidelines and literature search was planned every 5 years, given the clinical, molecular and therapeutic advances, including the use of biologic therapies. We present here updated guidelines that have been developed by a reorganized multidisciplinary group of international experts after systematic review of recent literature, discussions, and consensus reached at an expert conference held in June 2023. The guidelines provide summarized evidence and expert-based recommendations that aim to guide clinicians in the management of these rare and often complex diseases. These guidelines consist of two sections. This Part II covers the management of complications (eye, Ear-Nose-Throat, pruritus, pain, cutaneous infections, vaccinations, growth failure and nutritional deficiency, hair and nail anomalies, reaction to hot and cold climates, physical limitations, comorbidities) and the particularities of the neonatal period and Netherton syndrome.
AB - In 2019, a group of experts published the first European guidelines for the management of congenital ichthyoses after a multidisciplinary expert meeting held in 2016. An update of these guidelines and literature search was planned every 5 years, given the clinical, molecular and therapeutic advances, including the use of biologic therapies. We present here updated guidelines that have been developed by a reorganized multidisciplinary group of international experts after systematic review of recent literature, discussions, and consensus reached at an expert conference held in June 2023. The guidelines provide summarized evidence and expert-based recommendations that aim to guide clinicians in the management of these rare and often complex diseases. These guidelines consist of two sections. This Part II covers the management of complications (eye, Ear-Nose-Throat, pruritus, pain, cutaneous infections, vaccinations, growth failure and nutritional deficiency, hair and nail anomalies, reaction to hot and cold climates, physical limitations, comorbidities) and the particularities of the neonatal period and Netherton syndrome.
U2 - 10.1093/bjd/ljaf077
DO - 10.1093/bjd/ljaf077
M3 - Article
SN - 0007-0963
JO - British Journal of Dermatology
JF - British Journal of Dermatology
ER -