Abstract
Macrophage activation syndrome (MAS) is a secondary form of haemophagocytic lymphohistiocytosis (HLH). MAS-HLH is an underrecognised and life-threatening condition associated with a heterogeneous group of diseases including connective tissue disease and inflammatory disorders. Here, we report three cases of adult patients with MAS-HLH triggered by different entities, including systemic lupus erythematosus, Griscelli syndrome type 2, and Adult onset Still’s disease.
Original language | English |
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Pages (from-to) | 136-141 |
Number of pages | 6 |
Journal | Netherlands Journal of Medicine |
Volume | 78 |
Issue number | 3 |
Publication status | Published - 1 Apr 2020 |
Keywords
- Adults Still's disease
- Griscelli syndrome type 2
- haemophagocytic lymphohistiocytosis
- macrophage activation syndrome
- systemic lupus erythematosus
- MACROPHAGE ACTIVATION SYNDROME
- SYSTEMIC-LUPUS-ERYTHEMATOSUS
- COMBINED IMMUNODEFICIENCY
- REVERSION
- DISEASE
- MUTATION