Case series of three adult patients with exceptional clinical presentations of haemophagocytic lymphohistiocytosis

M. Khairoun, F. Meynen, W. Vercoutere, H. L. Leavis*

*Corresponding author for this work

Research output: Contribution to journalArticleAcademicpeer-review

Abstract

Macrophage activation syndrome (MAS) is a secondary form of haemophagocytic lymphohistiocytosis (HLH). MAS-HLH is an underrecognised and life-threatening condition associated with a heterogeneous group of diseases including connective tissue disease and inflammatory disorders. Here, we report three cases of adult patients with MAS-HLH triggered by different entities, including systemic lupus erythematosus, Griscelli syndrome type 2, and Adult onset Still’s disease.
Original languageEnglish
Pages (from-to)136-141
Number of pages6
JournalNetherlands Journal of Medicine
Volume78
Issue number3
Publication statusPublished - 1 Apr 2020

Keywords

  • Adults Still's disease
  • Griscelli syndrome type 2
  • haemophagocytic lymphohistiocytosis
  • macrophage activation syndrome
  • systemic lupus erythematosus
  • MACROPHAGE ACTIVATION SYNDROME
  • SYSTEMIC-LUPUS-ERYTHEMATOSUS
  • COMBINED IMMUNODEFICIENCY
  • REVERSION
  • DISEASE
  • MUTATION

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